Nutritional Management of Cystic Fibrosis
Cystic Fibrosis is an inherited disease that starts in utero. It is caused by a defective protein called the CF transmembrane conductance regulator (CFTR) and while the effects are seen throughout the body, changes in the lungs, gastrointestinal tract, pancreas and liver primarily impact nutritional...
সংরক্ষণ করুন:
| বিন্যাস: | Online |
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| ভাষা: | ইংরেজি |
| প্রকাশিত: |
MDPI - Multidisciplinary Digital Publishing Institute
2023
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| বিষয়গুলি: | |
| অনলাইন ব্যবহার করুন: | ONIX_20230623_9783036562674_65 |
| ট্যাগগুলো: |
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| _version_ | 1869517892705320960 |
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| collection | Directory of Open Access Books |
| description | Cystic Fibrosis is an inherited disease that starts in utero. It is caused by a defective protein called the CF transmembrane conductance regulator (CFTR) and while the effects are seen throughout the body, changes in the lungs, gastrointestinal tract, pancreas and liver primarily impact nutritional status. Survival and pulmonary function have been linked to nutritional status. Malnutrition and growth failure were historically the hallmark of disease. Patients with pancreatic insufficiency require pancreatic enzyme replacement therapy and fat-soluble vitamin supplements. With improvements in many areas including newborn screening, nutrition supplements, pancreatic enzymes, CFTR modulator drugs, inhaled antibiotics and mucolytics, life expectancy has increased. In this issue, we will review the latest information in children and adults regarding important factors that play a role in optimizing nutrition status, including body composition, the gut microbiome, food security, pancreatic enzyme replacement therapy, growth and bone health, and micronutrient abnormalities. Pediatric and adult providers both need to be aware of the nuances of care as more patients with CF become adults. Optimizing nutritional status, anticipating and preventing the complications of CF will result in best management practice. |
| format | Online |
| id | doab-20.500.12854ir-100833 |
| institution | Directory of Open Access Books |
| language | eng |
| publishDate | 2023 |
| publishDateRange | 2023 |
| publishDateSort | 2023 |
| publisher | MDPI - Multidisciplinary Digital Publishing Institute |
| publisherStr | MDPI - Multidisciplinary Digital Publishing Institute |
| record_format | ojs |
| spelling | doab-20.500.12854ir-1008332024-03-28T03:30:46Z Nutritional Management of Cystic Fibrosis Mascarenhas, Maria R. Alvarez, Jessica   Cystic Fibrosis  ；  Micronutrient  CF transmembrane conductance regulator；  Malnutrition  Gut microbiome  CF related diabetes  Bone health；  Body composition；  Diet；  Nutrition；  Exercise；  Physical Activity thema EDItEUR::G Reference, Information and Interdisciplinary subjects::GP Research and information: general thema EDItEUR::P Mathematics and Science::PS Biology, life sciences thema EDItEUR::J Society and Social Sciences::JB Society and culture: general::JBC Cultural and media studies::JBCC Cultural studies::JBCC4 Cultural studies: food and society Cystic Fibrosis is an inherited disease that starts in utero. It is caused by a defective protein called the CF transmembrane conductance regulator (CFTR) and while the effects are seen throughout the body, changes in the lungs, gastrointestinal tract, pancreas and liver primarily impact nutritional status. Survival and pulmonary function have been linked to nutritional status. Malnutrition and growth failure were historically the hallmark of disease. Patients with pancreatic insufficiency require pancreatic enzyme replacement therapy and fat-soluble vitamin supplements. With improvements in many areas including newborn screening, nutrition supplements, pancreatic enzymes, CFTR modulator drugs, inhaled antibiotics and mucolytics, life expectancy has increased. In this issue, we will review the latest information in children and adults regarding important factors that play a role in optimizing nutrition status, including body composition, the gut microbiome, food security, pancreatic enzyme replacement therapy, growth and bone health, and micronutrient abnormalities. Pediatric and adult providers both need to be aware of the nuances of care as more patients with CF become adults. Optimizing nutritional status, anticipating and preventing the complications of CF will result in best management practice. 2023-06-23T09:46:26Z 2023-06-23T09:46:26Z 2023 book ONIX_20230623_9783036562674_65 9783036562674 9783036562681 https://directory.doabooks.org/handle/20.500.12854/100833 eng image/jpeg Attribution 4.0 International https://mdpi.com/books/pdfview/book/7296 https://mdpi.com/books/pdfview/book/7296 MDPI - Multidisciplinary Digital Publishing Institute 10.3390/books978-3-0365-6268-1 10.3390/books978-3-0365-6268-1 46cabcaa-dd94-4bfe-87b4-55023c1b36d0 9783036562674 9783036562681 176 Basel open access |
| spellingShingle |   Cystic Fibrosis  ；  Micronutrient  CF transmembrane conductance regulator；  Malnutrition  Gut microbiome  CF related diabetes  Bone health；  Body composition；  Diet；  Nutrition；  Exercise；  Physical Activity thema EDItEUR::G Reference, Information and Interdisciplinary subjects::GP Research and information: general thema EDItEUR::P Mathematics and Science::PS Biology, life sciences thema EDItEUR::J Society and Social Sciences::JB Society and culture: general::JBC Cultural and media studies::JBCC Cultural studies::JBCC4 Cultural studies: food and society Nutritional Management of Cystic Fibrosis |
| title | Nutritional Management of Cystic Fibrosis |
| title_full | Nutritional Management of Cystic Fibrosis |
| title_fullStr | Nutritional Management of Cystic Fibrosis |
| title_full_unstemmed | Nutritional Management of Cystic Fibrosis |
| title_short | Nutritional Management of Cystic Fibrosis |
| title_sort | nutritional management of cystic fibrosis |
| topic |   Cystic Fibrosis  ；  Micronutrient  CF transmembrane conductance regulator；  Malnutrition  Gut microbiome  CF related diabetes  Bone health；  Body composition；  Diet；  Nutrition；  Exercise；  Physical Activity thema EDItEUR::G Reference, Information and Interdisciplinary subjects::GP Research and information: general thema EDItEUR::P Mathematics and Science::PS Biology, life sciences thema EDItEUR::J Society and Social Sciences::JB Society and culture: general::JBC Cultural and media studies::JBCC Cultural studies::JBCC4 Cultural studies: food and society |
| topic_facet |   Cystic Fibrosis  ；  Micronutrient  CF transmembrane conductance regulator；  Malnutrition  Gut microbiome  CF related diabetes  Bone health；  Body composition；  Diet；  Nutrition；  Exercise；  Physical Activity thema EDItEUR::G Reference, Information and Interdisciplinary subjects::GP Research and information: general thema EDItEUR::P Mathematics and Science::PS Biology, life sciences thema EDItEUR::J Society and Social Sciences::JB Society and culture: general::JBC Cultural and media studies::JBCC Cultural studies::JBCC4 Cultural studies: food and society |
| url | ONIX_20230623_9783036562674_65 |